Iso-Kikuchi syndrome; an overviewe

Congenital isolated Iso–Kikuchi syndrome in a newborn

Classic CO (also called Iso-Kikuchi syndrome) represents a benign, isolated condition associated with normal patient outcome. Nevertheless, clinical follow-up and/or further clinically-based tests are needed to exclude other nail diseases associated with multisystem pathology; complete family history is also important to determine sporadic or hereditary transmission of such condition.

Iso-Kikuchi syndrome with absence of ring fingers and metacarpal bone abnormality.

Neonate born to hepatitis B carrier mother presenting with congenital onychodysplasia of the index finger (Iso-Kikuchi syndrome).

Congenital onychodysplasia of the index fingers, also known as Iso–Kikuchi syndrome, is characterized using five diagnostic criteria: congenital occurrence, unilateral or bilateral involvement of the index fingers, variation in nail appearance, possible hereditary involvement and frequently associated bone abnormalities1–5. Herein, we present the case of a newborn with congenital onychodysplasi...

Kikuchi-Fujimoto disease* Doença de Kikuchi-Fujimoto

Kikuchi-Fujimoto disease is characterized by fever and lymphadenopathy, usually localized in the cervical region. This disease principally affects young females. It can be confused with lymphoma, adenocarcinoma metastasis and tuberculosis. We report two cases of KikuchiFujimoto disease. In the first case, a 28-year-old female had been treated for tuberculosis one year prior and presented with a...

Kikuchi-Fujimoto Disease in Patients with Sjögren’s Syndrome

Sjögren’s syndrome is a chronic autoimmune exocrinopathy associated with dry eyes and dry mouth as major clinical manifestations. It is characterized by lymphocytic infiltration of lacrimal and salivary glands and autoantibody production, especially anti-Ro (or SSA) and anti-La (or SSB). Lymphoproliferative disorders are a feature of Sjögren’s syndrome, and can be considered an extraglandular m...